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Hearingloss,preventionandmanagementHearingloss,preventionandmOverview
27,800,000hearingdisabilityinChinaIncidenceofhearinglossincreasingDeaf-mutismOverview27,800,000hearingdiHowtohear?GyritemporalestransversiAcousticradiationMedialgeniculatebodyNucleuscochlearisposteriorNucleuscochlearisanteriorSpiralorganofcortiLaterallemniscusSuperiorolivarynucleusAuditoryossiclesExternalacousticmeatusVestibularfenestraHowtohear?GyritemporalestWhyishearingveryimportant?MeanstorecognizetheworldFoundationtodevelopspeechAffectionsharing,lifeenjoyingImportantmeansofcommunicationWhyishearingveryimportant?ClassificationofhearinglossBynatureConductiveSensorineuralMixedBybirthCongenitalAcquired
Byspeechabilitywhendeaf-Prelingual-postlingualClassificationofhearingloss
NormalHearing
NormalHearing
ConductiveHearingLoss
ConductiveHearingLoss
SensorineuralHearingLoss
SensorineuralHearingLoss
MixedHearingLoss
MixedHearingLossLevelofHearinglossLeveldBHLNormal≤25dBHLMild26~40dBHLModerate41~70dBHLSevere71~90dBHLProfound﹥90dBHLLevelofHearinglossLeveldBHCommencausesofhearinglossCauseConductiveSensorineuralCongenitalEardeformityAntepartum:
heritage,bastardmeaslesAcquiredExternalear:cerumenotitisexternaforeignbodyMiddleear:otitismediawitheffusionchronicotitismediaotospongiosistraumaticperforationofeardrumbrokenossicularchainperinatalperiod:hypoxia,jaundiceototoxicity:aminoglycosides,cytotoxicDegeneration:presbycusisTrauma:noise,headinjury,surgeryTumor:acousticneuromaIdiopathic:Menieredisease,suddendeafnessInflammation:meningitis,measles,parotitisCommencausesofhearinglossC
CongenitalhearinglossandhereditaryhearinglossCongenitalhearingloss:hearingdisturbancewhenbirthHereditaryhearingloss:derivefromgeneorchromosomalanomaly
CongenitalhearinglossandhCongenitalhearinglossAntenatalperiod,circumnatalperiodorperinatalperiodCausesGeneticfactor:geneofdeafness,50%±Factorsduringpregnancy:earlyviralinfection,drugintoxication,noiseFactorsduringcircumnatalperiod:jaundice,lowbirthweightinfant,neonatalasphyxia,birthtraumaCongenitalhearinglossAntenatGeneofdeafness50%ofcongenitalhearinglossCommongenesofdeafnessGJB2SLC26A4(PDS)-enlargedvestibularaqueductsyndromeMutationofmitochondrialgeneGeneofdeafnessUniversalnewbornhearingscreening(UNHS)Toidentifyhearingdisturbancewithin3monthsUniversalnewbornhearingscreSignificanceofUNHSEarlydiscoveryofdeafnessmakesthedeafundumbPossibilityofearlydiscoveryRegistrationandmanagementforhighriskfamily
:only50%canbeidentifiedRoutinemedicalexamination:hardlyidentifiedwithin1yearoldParents’awareness:hardlyidentifiedwithin1yearoldUNHS
:effectivemethodSignificanceofUNHSEarlydisc
耳聲發(fā)射法快速腦干誘發(fā)電位法MethodofotoacousticemissionMethodofquickbrainstemevokedpotential耳聲發(fā)射法StrategyofUNHSscreeningrescreeningBirthFollowupInterventionRigorousFollowupDiagnosistestpasspassnormalNopassNopassNopassEvaluationpredischarge42天內(nèi)3月內(nèi)6月內(nèi)StrategyofUNHSscreeningrescrClinicalcharacteristicsofPresbycusis
hearingofoldage,theeffectsofagingProgressivehearinglossBilateralsymmetricsensorineuralhearinglossNohistoryofnoisecontactSpeechdiscriminationscorebadthanpuretonetestClinicalcharacteristicsofPr上海交通大學(xué)耳鼻咽喉科學(xué)英文版課件hearingloss,preventionandmanagement
Drug-inducedhearingloss,ototoxicityMechanismunclear,possibilyrelatedtodrugtype,dosage,route,geneticpredisposition,etc.
Drug-inducedhearingloss,ot
Ototoxicdrug(morethan90)AminoglycosideantibioticsAntitumordrug-cisplatin,carboplatinDiuretic-furosemide,ethacrynicacidSalicylate-aspirinantimalarialdrug-quininOtotoxicdrug(morethan90)Clinicalcharacteristicsof
ototoxicdeafnessBilateralhearinglossHearinglosshappensathighfrequencyReversibleorprogressiveWithtinitus,vertigoClinicalcharacteristicsof
oClinicalcharacteristicsof
noise-inducedhearinglossLongtermexposuretonoiseBilateralsymmetricEvidenthearinglossathighfrequency
:3-6kHzReversibleifseparatedfromnoiseProundhearinglossrareClinicalcharacteristicsof
nClinicalcharacteristics
ofidiopathicsuddenhearinglossSensorineuralhearinglosswithin3daysorless,morethan30dBHLUsuallyunilateralWithtinitus,vertigoEtiology:possibleviralinfectionanddisorderofbloodsupplyintheinnerearClinicalcharacteristics
ofiClinicalcharacteristics
ofacousticneuroma
Unilateralprogressivehearingloss,tinnitusClinicalcharacteristics
ofa
SystematicorinfectiousdiseasesKidneydiseaseDiabetesMeningitisViralinfectionSystematicorinfectiousdiseDiagnosisofhearinglossDetailedhistoryAge,time,symptomHistoryofusingototoxicdrug,familyhistoryofdeafness,historyofnoiseexposureExamination
:auralandgeneralExaminationofauditoryfunctionDiagnosisofhearinglossDetaiExaminationofauditoryfunction
PuretonetestSpeechaudiometryTympanogramandacousticreflectionAuditorybrainstemresponseOtoacousticemissionExaminationofauditoryfuncti上海交通大學(xué)耳鼻咽喉科學(xué)英文版課件hearingloss,preventionandmanagement上海交通大學(xué)耳鼻咽喉科學(xué)英文版課件hearingloss,preventionandmanagementImagingevaluation
HighdefinitionCTTemporalanatomyOsseousabnormalityFractureInfectiousdiseasesMagneticresonanceimaging(MRI)CerebellopontineangleVIIIcranialnerveLabyrinthImagingevaluationHighdefini上海交通大學(xué)耳鼻咽喉科學(xué)英文版課件hearingloss,preventionandmanagement上海交通大學(xué)耳鼻咽喉科學(xué)英文版課件hearingloss,preventionandmanagementProtectivemeasurefordeafnessPreventionofcongenitaldeafnessGeneticcounselingandprenataldiagnosisPregnantwomenareprohibitedtouseototoxicdrugsToavoidviralinfectionwhenpregnantPreventionofviralandbacterialinfectionMeaslesVaricellaParotitisEpidemicmeningitisRhinitisOtitismediaProtectivemeasurefordeafnesTokeepfavourablementalstatusandavoidover-tiredToavoidexposuretonoiseforlongtimeTolowerlevelofsoundsourceTodecreaseexposuretimeTouseearprotectorToprotectfromototoxicdeafnessTounderstandfamilyhistoryandsusceptivityTocontrolsuitabledosageandcourseoftreatmentProtectivemeasurefordeafnessTokeepfavourablementalstatManagementofhearinglossMedicine-corticosteroid,peripheralvasodilatorOtomicrosurgeryHearingaidCochlearimplantSpeechtrainingManagementofhearinglossMedi
Aimatsuddenorrecenthearingloss
CorticosteroidsPeripheralvasodilator
VitaminMedicaltherapy
AimatsuddenorrecentheariOtomicrosurgeryOtomi
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